Desmoplastic small round cell tumour (DSRCT) is a very rare malignant tumour which commonly presented as an
intraabdominal tumour. It has a distinct histological and immunophenotypic characteristic which differentiates it
from other types of small blue cell tumour such as Ewing’s sarcoma, primitive neuroectodermal tumour,
neuroblastoma and malignant mesothelioma. Apart from the abdomen, it may also originate from other region of the
body including the reproductive organs.