Mid-aortic syndrome (MAS) is a rare clinical entity that is
characterized by coarctation involving the distal thoracic and/or
abdominal aorta and its major branches accounting for 0.5–2%
of all cases of coarctation of the aorta (1). Renovascular
hypertension can be a significant sequelae - it is the main
symptomatic presentation of this disease among children and
adolescents. We describe a 9-year-old girl who presents with
recurrent abdominal pain and symptomatic hypertension. Due to
significant left ventricular systolic dysfunction and uncontrolled
hypertension, percutaneous balloon angioplasty was performed
to treat the coarctation. To our knowledge, this is the first
reported case of MAS in Malaysia. This case report highlights
the clinical presentation, the role of computed tomography
angiogram (CTA) in the diagnosis and current options in the
management of MAS.